| 沸点 | 191°C(lit.) |
| 别名 | ;["Glycerol α,α'-Diethyl Ether"] |
1,3-二乙氧基-2-丙醇
1,3-Diethoxy-2-propanol （订货以英文为准）
编号：D154147
CAS号：4043-59-8
分子式：C7H16O3
分子量：148.20
| 产品名称 | 1,3-Diethoxy-2-propanol |
| 中文名称 | 1,3-二乙氧基-2-丙醇 |
| CAS号 | 4043-59-8 |
| MDL编码 | D154147 |
| 分子式（M.F.） | C7H16O3 |
| 分子量（M.W.） | 148.20 |
| Reaxys-RN | 2209307 |
技术规格
| Background: | This gene is a member of the H/ACA snoRNPs (small nucleolar ribonucleoproteins) gene family. snoRNPs are involved in various aspects of rRNA processing and modification and have been classified into two families: C/D and H/ACA. The H/ACA snoRNPs also include the NOLA1, 2 and 3 proteins. The protein encoded by this gene and the three NOLA proteins localize to the dense fibrillar components of nucleoli and to coiled (Cajal) bodies in the nucleus. Both 18S rRNA production and rRNA pseudouridylation are impaired if any one of the four proteins is depleted. These four H/ACA snoRNP proteins are also components of the telomerase complex. The protein encoded by this gene is related to the Saccharomyces cerevisiae Cbf5p and Drosophila melanogaster Nop60B proteins. The gene lies in a tail-to-tail orientation with the palmitoylated erythrocyte membrane protein gene and is transcribed in a telomere to centromere direction. Both nucleotide substitutions and single trinucleotide repeat polymorphisms have been found in this gene. Mutations in this gene cause X-linked dyskeratosis congenita, a disease resulting in reticulate skin pigmentation, mucosal leukoplakia, nail dystrophy, and progressive bone marrow failure in most cases. Mutations in this gene also cause Hoyeraal-Hreidarsson syndrome, which is a more severe form of dyskeratosis congenita. Two transcript variants encoding different isoforms have been found for this gene. |
| Applications: | WB |
| Name of antibody: | DKC1 |
| Immunogen: | Fusion protein of human DKC1 |
| Full name: | dyskeratosis congenita 1, dyskerin |
| Synonyms： | DKC1; DKC; CBF5; DKCX; NAP57; NOLA4; XAP101 |
| SwissProt: | O60832 |
| WB Predicted band size: | 58 kDa |
| WB Positive control: | Hela and MCF7 cells |
| WB Recommended dilution: | 500-2000 |
搜索质检报告(COA)
搜索MSDS
相关产品
¥ 128.00
sh7651-500mL
¥ 128.00
sh8754-500mL
¥ 128.00
sh42798-500mL
¥ 128.00
sh54098-500mL
¥ 1470.00
PAC489Hu01-100μl
¥ 1756.00
MAB932Hu22-100μl
党沛 
